Nervous system (740) Anencephalus and similar anomalies (740.0) Anencephalus (741) Spina bifida (742) Other congenital anomalies of nervous system (742.1) Microcephalus (742.3) Hydrocephalus Eye, ear, face and neck (743) Congenital anomalies of eye (743.0) Anophthalmos (743.00) Clinical anophthalmos unspecified (743.03) Cystic eyeball congenital (743.06) Cryptophthalmos (743.1) Microphthalmos (743.2) Buphthalmos (743.3) Congenital cataract and lens anomalies (743.4) Coloboma and other anomalies of anterior segment (743.45) Aniridia (743.5) Congenital anomalies of posterior segment (743.6) Congenital anomalies of eyelids, lacrimal system, and orbit (744) Congenital anomalies of ear, face, and neck (744.0) Anomalies of ear causing impairment of hearing (744.1) Accessory auricle (744.2) Other specified congenital anomalies of ear (744.22) Macrotia (744.23) Microtia (744.3) Unspecified congenital anomaly of ear (744.4) Branchial cleft cyst or fistula; preauricular sinus (744.5) Webbing of neck (744.8) Other specified congenital anomalies of face and neck (744.81) Macrocheilia (744.82) Microcheilia (744.83) Macrostomia (744.84) Microstomia Circulatory system (745) Bulbus cordis anomalies and anomalies of cardiac septal closure (745.0) Common truncus (745.1) Transposition of great vessels (745.2) Tetralogy of fallot (745.3) Common ventricle (745.4) Ventricular septal defect (745.5) Atrial septal defect (745.6) Endocardial cushion defects (745.7) Cor biloculare (746) Other congenital anomalies of heart (746.1) Tricuspid atresia and stenosis congenital (746.2) Ebstein's anomaly (746.3) Congenital stenosis of aortic valve (746.4) Congenital insufficiency of aortic valve (746.5) Congenital mitral stenosis (746.6) Congenital mitral insufficiency (746.7) Hypoplastic left heart syndrome (746.8) Other specified congenital anomalies of heart (746.81) Subaortic stenosis congenital (746.82) Cor triatriatum (746.83) Infundibular pulmonic stenosis congenital (746.84) Congenital obstructive anomalies of heart not elsewhere cla**ified (746.85) Coronary artery anomaly congenital (746.86) Congenital heart block (746.87) Malposition of heart and cardiac apex (746.89) Other specified congenital anomalies of heart -Brugada syndrome (747) Other congenital anomalies of circulatory system (747.1) Coarctation of aorta (747.11) Interruption of aortic arch (747.2) Other congenital anomalies of aorta (747.3) Congenital anomalies of pulmonary artery (747.4) Congenital anomalies of great veins[disambiguation needed] (747.5) Absence or hypoplasia of umbilical artery (747.6) Arteriovenous malformation, unspec. (747.8) Other specified anomalies of circulatory system (747.81) Congenital anomalies of cerebrovascular system (747.82) Spinal vessel anomaly (747.83) Persistent fetal circulation (747.9) Unspecified congenital anomaly of circulatory system Respiratory system (748) Congenital anomalies of respiratory system (748.0) Choan*l atresia Digestive system (749) Cleft palate (749.0) Cleft palate, unspec. (749.2) Cleft palate w/ cleft lip (750) Other congenital anomalies of upper alimentary tract (750.0) Tongue tie (750.1) Other congenital anomalies of tongue (750.2) Other specified congenital anomalies of mouth and pharynx (750.3) Congenital tracheoesophageal fistula esophageal atresia and stenosis (750.4) Other specified congenital anomalies of esophagus (750.5) Congenital hypertrophic pyloric stenosis (750.6) Congenital hiatus hernia (750.7) Other specified congenital anomalies of stomach (750.8) Other specified congenital anomalies of upper alimentary tract (750.9) Unspecified congenital anomaly of upper alimentary tract (751) Other congenital anomalies of digestive system (751.0) Meckel's diverticulum (751.1) Congenital atresia and stenosis of small intestine (751.2) Imperforate an*s (751.3) Hirschsprung's disease (751.4) Congenital anomalies of intestinal fixation (751.5) Other congenital anomalies of intestine (751.6) Anomalies of gallbladder bile ducts and liver (751.7) Congenital anomalies of pancreas (751.8) Other specified congenital anomalies of digestive system (751.9) Unspecified congenital anomaly of digestive system Genital organs (752) Congenital anomalies of genital organs (752.0) Congenital anomalies of ovaries (752.1) Congenital anomalies of fallopian tubes and broad ligaments (752.2) Doubling of uterus (752.3) Other congenital anomalies of uterus (752.4) Anomalies of cervix, vagina, and external female genitalia (752.42) Imperforate hymen (752.5) Undescended testicle (752.6) Hypospadias and epispadias (752.61) Hypospadias (752.62) Epispadias (752.63) Congenital chordee (752.64) Micropenis (752.7) Indeterminate s** and pseudohermaphroditism Urinary system (753) Congenital anomalies of urinary system (753.0) Renal agenesis and dysgenesis (753.1) Cystic kidney disease (753.2) Obstructive defects of renal pelvis and ureter (753.3) Other specified anomalies of kidney -Renal ectopia -Horseshoe kidney (753.4) Other specified anomalies of ureter -Ectopic ureter (753.5) Exstrophy of urinary bladder (753.6) Atresia and stenosis of urethra and bladder neck (753.7) Anomalies of urachus -Urachal cyst (753.8) Other specified anomalies of bladder and urethra (753.9) Unspecified anomaly of urinary system Musculoskeletal system (754) Certain congenital musculoskeletal deformities (754.1) Torticollis, sternomastoid (754.3) Dislocation of hip, unilateral (754.5) Varus deformities of feet (754.51) Talipes equinovarus (754.6) Valgus deformities of feet (754.8) Other specified nonteratogenic anomalies (754.81) Pectus excavatum (755) Other congenital anomalies of limbs (755.0) Polydactyly (755.1) Syndactyly (755.5) Other congenital anomalies of upper limb including shoulder girdle (755.54) Madelung's deformity (755.55) Acrocephalosyndactyly -Apert syndrome (755.9) Limb anomaly, unspec. (756) Other congenital musculoskeletal anomalies (756.1) Anomalies of spine (756.12) Spondylolisthesis (756.16) Klippel-Feil syndrome (756.17) Spina bifida occulta (756.2) Cervical rib (756.3) Other congenital anomalies of ribs and sternum (756.4) Chondrodystrophy (756.5) Osteodystrophies (756.51) Osteogenesis imperfecta (756.6) Congenital anomalies of diaphragm (756.7) Congenital anomalies of abdominal wall (756.8) Other specified congenital anomalies of muscle tendon fascia and connective tissue (756.81) Congenital absence of muscle and tendon (756.82) Accessory muscle (756.83) Ehlers-Danlos syndrome Integument (757) Congenital anomalies of the integument (757.3) Other specified anomalies of skin (757.32) Birthmarks (757.39) Other specified congenital anomalies of skin -Bloom syndrome -Epidermolysis bullosa -Pseudoxanthoma elasticum (757.6) Supernumerary nipple Chromosomal anomalies (758) Chromosomal anomalies (758.0) Down syndrome (758.1) Patau's syndrome (758.2) Edward's syndrome (758.3) Autosomal deletion syndromes (758.31) Cri du chat (758.32) Velo-cardio-facial syndrome (758.33) Other microdeletions -Miller-Dieker syndrome -Smith-Magenis syndrome (758.4) Balanced autosomal translocation in normal individual (758.5) Other conditions due to autosomal anomalies (758.6) Gonadal dysgenesis -Turner's syndrome -XO syndrome (758.7) Klinefelter's syndrome (758.8) Other conditions due to s** chromosome anomalies (758.9) Conditions due to anomaly of unspecified chromosome Other (759) Other and unspecified congenital anomalies (759.0) Anomalies of spleen, congenital (759.1) Anomalies of adrenal gland, congenital (759.2) Anomalies of other endocrine glands, congenital (759.3) Situs inversus (759.4) Conjoined twins (759.5) Tuberous sclerosis (759.6) Other congenital hamartoses, not elsewhere cla**ified -Cowden syndrome (759.7) Multiple congenital anomalies, so described (759.8) Other specified congenital anomalies (759.81) Prader-Willi syndrome (759.82) Marfan syndrome (759.83) Fragile X syndrome (759.89) Other specified congenital anomalies (759.9) Congenital anomaly, unspecified